Primary antiphospholipid syndrome presenting as gross communicating hydrocephalus

Authors

  • Dibya Ranjan Behera IMS,BHU
  • Nand Kumar Singh BHU
  • Manoj Godara

DOI:

https://doi.org/10.15305/ijrci/v1i1/24

Keywords:

Primary antiphospholipid syndrome, communicating hydrocephalus, headache

Abstract

Primary antiphospholipid syndrome (APS) presents with a wide variety of neurological syndromes. But, hydrocephalus is seen very rarely. We report a case of gross communicating hydrocephalus in a 20-year-old woman with primary APS presented with headache and blurring of vision, without any focal neurologic signs. Magnetic resonance venography revealed superior sagittal sinus and bilateral cortical vein thrombosis.

Author Biographies

Dibya Ranjan Behera, IMS,BHU

Junior resident

General Medicine

IMS, BHU

Nand Kumar Singh, BHU

Professor of Medicine and Head Division of RHeumatology,

Institute of Medical Sciences, BHU,

Varanasi

Manoj Godara

Junior resident

General Medicine

IMS, BHU

References

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Wani AM, Hussain WM, Fatani MI, Qadmani A, Maimani GAA, Turkistani A, et al. Lower cranial nerve palsy, aseptic meningitis and hydrocephalus: unusual presentation of primary antiphospholipid syndrome. BMJ Case Rep. 2009;2009.

Miyakis S, Lockshin MD, Atsumi T, Branch DW, Brey RL, Cervera R, et al. International consensus statement on an update of the classification criteria for definite antiphospholipid syndrome (APS). J. Thromb. Haemost. 2006 Feb;4(2):295–306.

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Published

26-02-2013

Issue

Vol. 1 No. 1 (2013)

Section

Case Studies

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