Rowell Syndrome: A case report and review of literature

Authors

  • Anuj Sharma Regional Hospital, Bilaspur, Himachal Pradesh, India.
  • Reena Sharma Regional Hospital, Bilaspur, Himachal Pradesh, India

DOI:

https://doi.org/10.15305/ijrci/v4i1/202

Keywords:

Rowell syndrome, Lupus erythematosus, Erythema multiformae, Speckled ANA.

Abstract

Rowell syndrome is a rare disease consisting of lupus erythematosus associated with erythema multiforme-like lesions. The present case study discusses the occurrence of this syndrome in a 38-year-old female who presented with erythematous scaly lesions on face, neck and back, along with the targetoid lesions on upper arms and back of the neck, with oral erosions. Laboratory investigations revealed speckled pattern of anti-nuclear antibody (ANA) with a titer of 1:640, and anti-dsDNA and anti-La (SS-B) positivity. Histology of the targetoid lesion was consistent with erythema multiforme. Significant improvement within four weeks was noted with the use of oral steroids and anti-malarials.

 

Author Biographies

Anuj Sharma, Regional Hospital, Bilaspur, Himachal Pradesh, India.

Specialist Medical Officer, Department of Dermatology.

Reena Sharma, Regional Hospital, Bilaspur, Himachal Pradesh, India

Specialist Medical Officer, Department of Dermatology.

References

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Published

01-10-2016

Issue

Vol. 4 No. 1 (2016)

Section

Case Studies

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